Table 1. Classification of diseases by disease subtype and sex in fatal cases.
| Classification | sCJD (n = 674) | fCJD (n = 93) | dCJD (n = 63) | GSS (n = 20) | FFI (n = 3) | |||||
| Male (n = 293) |
Female (n = 381) |
Male (n = 43) |
Female (n = 50) |
Male (n = 22) |
Female (n = 41) |
Male (n = 8) |
Female (n = 12) |
Male (n = 2) |
Female (n = 1) |
|
| Definite | 46 (15.7%) | 44 (11.5%) | 11 (25.6%) | 14 (28.0%) | 11 (50.0%) | 17 (41.5%) | 2 (25.0%) | 0 | 2 (100%) | 1 (100%) |
| Probable | 230 (78.5%) | 314 (82.4%) | 32 (74.4%) | 33 (66.0%) | 8 (36.4%) | 15 (36.6%) | 6 (75.0%) | 11 (91.7%) | 0 | 0 |
| Possible | 17 (5.8%) | 23 (6.0%) | 0 | 3 (6.0%) | 3 (13.6%) | 9 (22.0%) | 0 | 1 (8.3%) | 0 | 0 |
Abbreviations: sCJD, sporadic Creutzfeldt-Jakob disease; fCJD, familial CJD; dCJD, CJD acquired from cadaveric dura mater grafts; GSS, Gerstmann-Sträussler-Sheinker syndrome; FFI, fatal familial insomnia.