Table 2.
Pat. | First symptoms | Sitting ability | Walking ability | Scoliosis (Cobb degree) | Pelvic tilt | Hip joint involvement contractures, feet deformities |
Orthopedic surgeries | Age of surgery (years) |
---|---|---|---|---|---|---|---|---|
1 | LW | Yes | Yes | Incipient, <10° | — | — | Hip-TEP left | 59 |
2 | LW | Yes | Yes | — | — | — | Reconstruction of rotator cuff right | 50 |
3 | GW | Yes | Yes | Th: right-conv. 26° Th3/Th7/Th11 | — | — | — | — |
4 | IMD | No | Limited2 | Th/L: right-conv. C-shaped 80° Th5/Th11/L5 | 40° right | Hip dysplasia/luxation right Pes equinus |
Intertrochanteric varus osteotomy right | 17 |
5 | IMD | Yes1 | No | Th: right-conv. 57° Th1/Th8/Th124; L: left-conv. 90° L1/L3/L54 |
35° left | Hip dysplasia/luxation left + right Hip + knee flexor contractures Pes planovalgus |
Spine stabilization Th3-S1 Post-op: Th 38°, L 23°, pelvic tilt 0° |
14 |
Derotating varus osteotomy both sides; hip and knee flexor release left+right | 13 | |||||||
6 | LW | Yes | No3 | Th/L: right-conv. C-shaped 90° Th6/L1/L5 | 40° right | Hip dysplasia left + right Hip + knee flexor contractures |
Spine stabilization Th3-S1 Post-op: Th 35°, pelvic tilt 8° |
13 |
Hip and knees flexor release left + right | 4 | |||||||
7 | LW | No | No | Th/L: left-conv., collapsing spine5 | 60° left | Talipes equinovarus | Surgery not possible6 | — |
8 | IMD | Yes | Yes | — | — | Pes equinus | Achillotenotomy left + right | 5 |
Pat.: patient, LW: leg weakness, GW: general weakness, IMD: impaired motor development, left-conv.: left-convex, right-conv.: right-convex, Th: thoracic, and L: lumbar. 1was lost due to scoliosis and pelvic obliquity and regained after spine stabilization surgery. 2Only transfer walking for a few meters inside. 3Ability lost at the age of 13 years. 4Last examination before surgery. 5Cobb degree not measurable and sitting position for X-ray is not achievable. 6Operative stabilization was indicated; patient's general condition is not sufficient for surgery.