Table 1. Clinical features of world’s 14 cases of primitive neuroectodermal tumors of the pancreas (1-5).

Case No.	Age (years)	Sex	Presenting symptoms	Size (cm)	Cytogenetic analysis	Diagnosis procedure	Treatment	Metastasis	Clinical follow-up
1	17	M	Jaundice, Abdominal pain	9.0	+	Whipple resection	CHE	N/A	33 mo; NED
2	20	M	Jaundice, Abdominal pain	3.5	+	Whipple resection	N/P	N/A	27 mo; AWD
3	25	F	Abdominal pain	N/A	N/A	Biopsy	N/A	N/A	N/A
4	21	F	Abdominal pain	N/A	+*	Whipple resection	N/A	N/A	DOC
5	25	F	Jaundice, Abdominal pain	8.0	-*	Biopsy	N/A	N/A	N/A
6	13	M	Abdominal pain	6.0	N/A	Biopsy	N/A	N/P	43 mo; NED
7	6	M	Jaundice, Abdominal pain	3.5	+*	Whipple resection	CHE	48 mo; Recurrence	48 mo; DOD
8	31	M	Abdominal pain fever	10.0	-	Whipple resection	RAD CHE	4 mo, Recurrence; 24 mo/36 mo, lung	50 mo; DOD
9	6	F	Abdominal pain Anemia	5.5	-**	Whipple resection	N/P	6 mo;Recurrence	6 mo; DOD
10	13	F	Dyspepsia Vomiting	22	N/A	Whipple resection	CHE	N/A	N/A
11	31	M	Abdominal pain Loss of appetite	N/A	N/A	Biopsy	CHE	N/A	N/A
12	17	M	Abdominal pain	9	+	Whipple resection #	RAD CHE	N/P	8 mo; AWD
13	33	M	Abdominal pain	15	+	Laparotomy	RAD CHE	Simultaneously, liver, spleen	12 mo;AWD
14#	13	F	Abdominal pain Diabetes mellitus 2	3.5	+	RUPT	RAD CHE	9/36 mo, Recurrence; 12 mo, ascites	41 mo; AWD

Sex, M, male; F, female; N/A, not available; N/P, not performed; Cytogenetic analysis (+), t[11;22][q24;12]; *RT-PCR, reverse transcriptase Polymerase Chain Reaction data; RUPT, resection of the uncinate process tumor, preserving the duodenum; #Whipple resection, pylorus preserving pancreatoduodenectomy; -**, loss of cosmids F7 and E4 distal of the EWSR1 breakpoint in nearly all cells; NED, no evidence of disease; AWD, alive with disease; DOC: died of postoperative complications; DOD, died of disease; mo, month; Metastasis, post operation time and position of the metastasis; RAD, radiotherapy; CHE, chemotherapy; ^#14 our case