Table 1. Diagnosis [pathology].
Diagnosis: pathology | Adult, No. [%] | Pediatric, No. [%] |
---|---|---|
Cirrhosis | 14,685 [72.27] | 168 [31.34] |
Tumor [not associated with cirrhosis] | 2,152 [10.59] | 21 [3.92] |
Graft failure | 596 [2.93] | 11 [2.05] |
CAH | 555 [2.73] | 1 [0.19] |
Fulminant hepatic failure | 550 [2.71] | 13 [2.43] |
Chronic liver disease [CAH or cirrhosis] | 497 [2.45] | 0 [0] |
Primary biliary cirrhosis | 360 [1.77] | 24 [4.48] |
CAH acute flare | 270 [1.33] | 1 [0.19] |
Cirrhosis with acute deterioration or complications | 148 [0.73] | 2 [0.37] |
Polycystic disease | 76 [0.37] | 1 [0.19] |
Secondary biliary cirrhosis | 63 [0.31] | 3 [0.56] |
Primary sclerosing cholangitis | 51 [0.25] | 2 [0.37] |
Budd-Chiari syndrome | 45 [0.22] | 3 [0.56] |
Other metabolic disease | 43 [0.21] | 38 [7.09] |
Biliary atresia | 14 [0.07] | 199 [37.31] |
Familial amyloidotic polyneuropathy | 5 [0.02] | 1 [0.19] |
Unspecified | 210 [1.03] | 48 [8.96] |
Total | 20,320* [100] | 536* [100] |
*Excluded cases (Adult: missing N=17; Pediatric: missing N=4) with missing pathological diagnosis