Table 1.

Reported cases of CLIPPERS^*.

Author/source	Country	Cases	Sex		Biopsies
			Male	Female
Pittock et al. [1]	United States and Belgium	8	3	5	4
Duprez and Sindic [20]	Belgium	1	–	1	–
Gabilondo et al. [19]	Spain	1	–	1	–
Jones et al. [21]	United Kingdom	1	–	1	1
Kastrup et al. [10]	Germany	3	3	–	3
List et al. [17]	Germany	1	–	1	–
Huhn and Obermann [13]	Germany	1	1	–	1
Taieb et al. [18]	France	1	1	–	1
Biotti et al. [22]	France	1	1	–	–
Lefaucheur et al. [23]	France	1	1	–	–
Simon et al. [7]	Australia	5	4	1	5
Taieb et al. [2]	France	12	9	3	7
Sczesni et al. [12]	Germany	1	1	–	–
Humbroich et al. [25]	Germany	1	1	–	–
Hillesheim et al. [9]	United States	1	1	–	1
Tohge et al. [11]	Japan	1	–	1	–
Sempere et al. [24]	Spain	1	1	–	–
Wetter et al. [26]	Germany	1	1	–	1
Wijntjes et al. [27]	Netherlands	1	1	–	–
Sonoda et al. [48]	Japan	1	1	–	–
Safdieh et al. [28]	United States	5	4	1	5
Maddison et al. [49]	United Kingdom	1	n.r.	n.r.	–
Egelseer et al. [8]	Germany	1	1	–	–
Mann et al. [40]	Germany	1	1	–	–
Hidarilak et al. [39]	United States	1	–	1	–
Al-Mufti et al. [50]	United States	1	–	1	–
Tarabishy et al. [51]	United States	1	n.r.	n.r.	–
Pesaresi et al. [52]	Italy	1	1	–	–
Total		56	37 (+2)†	17 (+2)†	29

^*Reports of extraordinary and mimicking cases of CLIPPERS (chronic lymphocytic inflammation with pontine perivascular enhancement responsive to steroids) were not included in this table. In addition to some extraordinary cases of CLIPPERS (Ortega et al. [29], Ferreira et al. [34], Buttmann et al. [32]), several presumptive cases of CLIPPERS were reported, in which other discrete diseases were finally diagnosed (Limousin et al. [30], De Graaff et al. [31], Jones et al. [21]).

^†In two cases sex of the affected patient was not identifiable; n.r.: not reported.