Table 1.
Human conditions of unknown cause that map to defined genetic regions encompassing the six CCPs; CCP1 - CCP6.
Condition | OMIM | Band Interval | Encoding gene |
---|---|---|---|
Spastic Paraplegia-19 | 607152 | 9q33-q34 | CCP1, AGTPBP1 |
Spastic Paraplegia-41 | 613364 | 11p14.1-p11.2 | CCP2, AGBL2 |
Spinocerebellar ataxia-32 | 613909 | 7q32-q33 | CCP3, AGBL3 |
Primary ciliary dyskinesia-8 | 612274 | 15q24-q25 | CCP4, AGBL1 |
Essential hereditary tremor-2 | 602134 | 2p25-p22 | CCP5, AGBL5 |
Dystonia-9: episodic ataxia & spasticity | 601042 | 1p33 | CCP6, AGBL4 |