Table 1.
Baseline characteristics of patients with Becker muscular dystrophy
| Exon Deletion | Age, at study, years | Age at onset of symptoms, years | Age at loss of ability to run, years | Maximum voluntary contraction (grip strength) | CK level, IU/L | Frequency of wheelchair/scooter use | Medications | ||
|---|---|---|---|---|---|---|---|---|---|
| right arm, kg | left arm, kg | ||||||||
| P1 | 45–48 | 32 | 5 | 18 | 32 | 22 | 1883 | never | none |
| P2 | 45–48 | 33 | 5 | 22 | 23 | 29 | 1247 | never | none |
| P3 | 45–48 | 42 | 30 | 30 | 42 | 39 | 719 | never | none |
| P4 | 45–55 | 38 | 12 | 26 | 29 | 23 | 2006 | never | none |
| P5 | 45–48 | 42 | 28 | 32 | 29 | 33 | 1453 | rarely | none |
| P6 | 48–49 | 38 | 25 | 27 | 35 | 33 | 2058 | never | none |
| P7 | 67 | 50 | 32 | 38 | 36 | 42 | 2247 | rarely | oxybutynin |
| P8 | 20–29 | 30 | 12 | 15 | 13 | 10 | 3745 | never | deflazacort |
| P9 | 14–44 | 50 | 33 | 35 | 21 | 17 | 707 | never | none |
| P10 | 3–7 | 19 | 6 | 8 | 13 | 12 | 2448 | often | none |
P, patient; CK, creatine kinase