Table 1.
Criterion | Description |
---|---|
1. Epistaxis | Spontaneous recurrent nosebleeds |
2. Mucocutaneous telangiectasia | Multiple at characteristic sites: fingertip pulps, lips, oral cavity |
3. Visceral involvement | Gastrointestinal, pulmonary, hepatic, cerebral or spinal AVM |
4. Family history | A first-degree relative affected according to these criteria |
The HHT diagnosis is classified as:
Definite: three criteria are present.
Possible or suspected: two criteria are present.
Unlikely: fewer than two criteria are present.