Table 1.
Patient Data
Gender | |
Male | 7 pts |
Female | 8 pts |
Age | |
Median Age (overall) | 45 y |
Median Age (Adults) | 51 y |
Range (Adults) | 23–59 y |
Median Age (Children) | 4.9 y |
Range (Children) | 3.6–14.8 y |
Prior Therapies | |
Steroids | 4 pts |
CHOP/CHOP-like | 4 pts |
Autologous Transplant | 1 pts |
None | 6 pts |
Disease Description | |
History of HPS | 0 pts |
Dose of Bexarotene | |
Median Dose (Adults) | 300 mg |
Range of Dose (Adults) | 75–675 mg |
Median Dose (Children) | 130 mg/m2 |
Range of Dose (Chidren) | 119–308 mg/m2 |
Abbreviations: CHOP = cyclophosphamide, adriamycin, vincristine, prednisone regimen; HPS = hemophagocytic syndrome.