Table 1. Demographic and clinical characteristics of 381 patients with systemic sclerosis*.
Age, years, median (IQR) | 57 (47–65) |
Age at disease onset, years, median (IQR) | 46 (38–55) |
Male sex | 62/379 (16.4) |
Patient association | 62/191 (32.5) |
Disease duration, years, median (IQR) | 7 (3–13) |
Body mass index, kg/m2, median (IQR) | 23 (20–26) |
Diffuse cutaneous SSc | 149/370 (40.3) |
Limited cutaneous SSc | 187/370 (50.5) |
Limited SSc | 34/370 (9.2) |
KPS (0–100), median (IQR) | 80 (70–90) |
Inter-incisor distance, mm, median (IQR) | 36 (30–40) |
Skin involvement | 339/370 (91.6) |
Telangiectasia | 253/347 (72.9) |
Raynaud’s phenomenon | 369/377 (97.9) |
Pitting scars | 221/376 (58.8) |
Digital ulcers | 170/375 (45.3) |
Calcinosis | 105/312 (33.7) |
Gastrointestinal tract involvement | 304/375 (81.1) |
Arthralgia | 254/375 (67.7) |
Myalgia | 209/375 (55.7) |
Dyspnea, NYHA classification, median (IQR) | 2 (2–3) |
Interstitial lung disease | 163/373 (43.7) |
Echocardiography systolic PAP>35 mmHg | 48/375 (12.8) |
Scleroderma renal crisis | 34/375 (9.1) |
*Values are number/number of patients for whom the data is available (%), otherwise indicated.
IQR: interquartile range; KPS: Karnofsky performance status; NYHA: New York Heart Association; PAP: pulmonary artery pressure.