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. Author manuscript; available in PMC: 2015 Mar 1.
Published in final edited form as: Paediatr Respir Rev. 2013 Nov 15;15(1):4–12. doi: 10.1016/j.prrv.2013.11.003

Table 2.

Examples of distribution of SCD genotypes in various parts of the world

Dakar,
Senegal (14)
(univ. hosp.)
age* 1–10+
n = 556
Zaria,
Nigeria (15)
(univ. hosp.)
age 10–52
n = 208
Ibadan,
Nigeria (16)
(univ. hosp.)
age 3–16
n = 145
Ouagadougou,
Burkina Faso (18)
(urban hosp.)
age 1–42
n = 387
Ouagadougou,
Burkina Faso (17)
(screening)
age 1–30
n = 153
Greece
National
Registry (19)
---
n = 1080
Riyadh, Saudi
Arabia (38)
(univ. hospital)
age 1–69
n = 159
Andhra Pradesh,
India (21)
(screening)
---
N = 78
Chennai,
India (20)
(urban hosp.)
---
n = 22
Hb SS 95.7% 95.2% 87.6% 50.4% 7.8% 19.0% 71.7% 67.9% 36.4%
Hb SC 3.6% 4.8% 12.4% 49.6% 92.2% --- --- --- ---
Hb Sβ-thal 0.7% --- --- --- --- 81.0% 28.3%1 30.8% 63.6%
Hb SD --- --- --- --- --- --- --- 1.3%
*

age given in years

1

26.4% Hb Sβ0-thalassemia; 0.2% Hb Sβ+-thalassemia