Table 2.
Individual absolute urinary oxalate levels and response depending on administered dosage during study weeks 0–24
| Patient | Uox Level per Vitamin B6 Dosage (mmol/1.73 m2 per day) | Genotype | ||||||||
|---|---|---|---|---|---|---|---|---|---|---|
| Baseline (Vitamin B6, 0 mg/kg per day) | Study Week 6 (Vitamin B6, 5 mg/kg per day) | Study Week 12 (Vitamin B6, 10 mg/kg per day) | Study Week 18 (Vitamin B6, 15 mg/kg per day) | Study Week 24 (Vitamin B6, 20 mg/kg per day) | ||||||
| Uox | Response | Uox | Response | Uox | Response | Uox | Response | |||
| 01 | 2.05 | 1.20 | + | 1.25 | + | 0.95 | + | 1.05 | + | c.508G>A; c.959_960delCA |
| 02 | 1.70 | 1.30 | − | 2.0 | − | 2.25 | − | 1.25 | − | c.508G>A; c.959_960delCA |
| 03 | 2.35 | 1.25 | + | 1.45 | + | 1.20 | + | 1.95 | − | c.508G>A; c.364C>T |
| 04 | 2.10 | 2.60 | − | 2.15 | − | 2.85 | − | 2.4 | − | c.33delC; c.33delC |
| 05 | 1.90 | 1.20 | + | 1.35 | − | 1.50 | − | 1.8 | − | c.454T>A; c.1151T>C |
| 06 | 1.65 | 1.05 | + | 0.68 | + | 1.00 | + | 0.9 | + | c.508G>A; c.508G>A |
| 07 | 2.25 | 0.75 | + | 1.00 | + | 1.20 | + | 1.00 | + | c.508G>A; c.508G>A |
| 08 | 3.50 | 2.80 | − | 2.75 | − | 2.25 | + | 1.65 | + | c.327delG; c.327delG |
| 09 | 2.31 | 1.20 | + | 1.30 | + | 1.60 | + | 1.35 | + | c.560C>T; c.836T>C |
| 10 | 2.30 | 2.80 | − | 2.60 | − | 2.85 | − | 2.75 | − | c.482G>A; c.976 del G |
| 11 | 1.45 | 1.05 | − | 1.00 | + | 0.85 | + | 1.35 | − | c.508G>A; c.847-3C>G |
| 12 | 1.50 | 1.02 | + | 0.60 | + | 1.05 | − | 0.90 | + | c.508G>A; c.508G>A |
Uox, urinary oxalate.