TABLE 2.

Comparison of type 1 and type 2 autoimmune pancreatitis (AIP)

Feature	Type 1 AIP	Type 2 AIP
Age	Elderly	Young
Clinical presentation	Painless jaundice	Obstructive jaundice ± acute pancreatitis
Histology	Periductal lymphoplasmacytic infiltrate; Storiform fibrosis; Obliterative phlebitis	Granulocytic epithelial lesion
Serum IgG	Elevated in 80% of cases	Normal
IgG4-related diseases	Yes	No
Association with IBD	Rare	Yes, found in 16% of cases
Response to steroids	Yes	Yes
Relapse	Common	Rare

Adapted from reference 8. IBD Inflammatory bowel disease; IgG Immunoglobulin G