Table 1.
Showing clinicopathological features of 21 cases of pediatric sclerosing rhabdomyosarcomas reported in the literature (including present case).
| Case number | Author | Year | Age/ sex |
Site | Size (cm) | Mets (1) | Primary Rx | Adj. Rx |
Local recurrence | Mets (2) | TTR/TTM (mos) |
Rx of Rec/Mets | F/U (mos) |
Outcome |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | Folpe et al. [8] | 2002 | 18/M | Orbit | NA | (−) | Excision | (−) | (−) | Intra-abdominal and lymph nodes | 48 | CT | 60 | Died |
|
| ||||||||||||||
| 2 | Vadgama et al. [9] | 2004 | 3/F | Ischiorectal fossa/buttock | 3.2 | (−) | Excision | CT | (−) | (−) | (−) | (−) | 4 | AWD |
|
| ||||||||||||||
| 3 | Chiles et al. [7] | 2004 | 6/M | Arm | NA | NA | NA | NA | (+) | (−) | 20 | NA | 39 | Alive with disease |
| 4 | 11/M | Elbow | NA | (−) | NA | NA | (−) | (+) | 20 | NA | 37 | Dead | ||
| 5 | 7/F | Pharynx | NA | (−) | NA | NA | (+) | (−) | 4 | NA | 16 | Alive with disease | ||
| 6 | 10/F | Orbit | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | 18 | AWD | ||
| 7 | 3/M | Leg | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | 10 | AWD | ||
| 8 | 8/F | Sinus | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | <1 | AWD | ||
| 9 | 16/F | Thigh | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | 25 | AWD | ||
| 10 | 4/F | Scapula | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | NA | NA | ||
| 11 | 12/M | Masseter | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | <1 | AWD | ||
| 12 | 9/M | Orbit | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | 43 | AWD | ||
| 13 | 4/M | Neck | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | 37 | AWD | ||
| 14 | 0.3/M | Retroperitoneum | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | NA | NA | ||
| 15 | 5/M | Scrotum | NA | (−) | NA | NA | (−) | (−) | (−) | (−) | 24 | AWD | ||
|
| ||||||||||||||
| 16 | Zambrano et al. [11] | 2006 | 8/F | Intra-abdominal | 10.5 | (−) | CT f/b Excision | (−) | NA | NA | NA | NA | NA | NA |
| 17 | 18/M | Thigh | NA | NA | NA | NA | NA | NA | NA | NA | NA | NA | ||
| 18 | 17/M | Lower leg | 9.0 | NA | CT f/b Excision | NA | NA | NA | NA | NA | NA | NA | ||
|
| ||||||||||||||
| 19 | Wang et al. [10] | 2008 | 12/F | Nasal cavity | 4.0 | (−) | Excision | (−) | (+) | (−) | 3 | Excision + CT | 5 | AWD |
|
| ||||||||||||||
| 20 | Bouron-Dal Soglio et al. [6] | 2009 | 7/M | Deltoid | 3.7 | (−) | Excision | CT | (+) | Lung, Lymph nodes | 24 | Excision + SCT | 72 | Alive with Disease |
|
| ||||||||||||||
| 21 | Present case | 2013 | 11/M | Skull base | 9.3 | (−) | Excision | CT + RT | (+) | Spinal leptomeningeal | 14 | RT + CT | 16 | Alive with Disease |
AWD: alive without disease; CT: chemotherapy; RT: radiotherapy; NA: not available; Mets (1): metastases at presentation; Mets (2): metastases during follow-up; Adj.: adjuvant; Rx: treatment; f/b: followed by; SCT: stem cell transplantation; mos: months; Rec: recurrence; TTR: time to recurrence; TTM: time to metastases.