Littermates from all four genotypes (n=4/group) were assessed at 60 weeks of age for expression of specific neurotransmitter receptors in different brain regions, measured by autoradiography. As previously reported [27], compared to wild type mice HdhQ200 mice show a significant decrease in D1 receptor binding in striatum, nuclear accumbens (nAcc) and olfactory tubercle (Olf Tub). A significant increase in striatal GABAA receptor binding in HdhQ200 mice has not been previously reported. One-way ANOVA with Bonferroni post hoc established that D1 receptor (A, B), D2 receptor (data not shown) and GABAA receptor (C, D) expression does not differ significantly between HdhQ200/Atxn3+/+ and HdhQ200/Atxn3-/- mice. Error bars represent SEM. *p<0.05, **p<0.01, ***p<0.001 and ns = no significance.