Table 2.
Patient | Surgery | Diagnosis | Outcome |
---|---|---|---|
1 | TCPC - extracardiac, fenestrated; and, L pulmonary arteryplasty | HLHS | Fontan circulation taken down after return to the OR on POD 1 because of failed Fontan circulation. Unable to separate from CPB; placed on ECLS. |
2 | TCPC - extracardiac, fenestrated; and, R atrial maze, R atrial reduction, oversew of pulmonary valve | Ebstein’s anomaly-HRV | Fontan circulation taken down in the OR because of failed Fontan circulation, unable to separate from CPB; another MBTS was added in the same operation. |
3 | TCPC - extracardiac, fenestrated; and, focalization of hepatic veins | Unbalanced AVSD | Fontan circulation taken down 11 mo after operation because of poor hemodynamics requiring prolonged and frequent PCICU hospitalizations and the ultimate development of PLE; also had ECLS during the postoperative course of TCPC because of profound LCOS at PODs 2–5. |
TCPC, total cavopulmonary connection; POD, postoperative day; HLHS, hypoplastic left heart syndrome; HRV, hypoplastic right ventricle; AVSD, atrioventricular septal defect; OR, operating room; CPB, cardiopulmonary bypass; PLE, protein-losing enteropathy; ECLS, extracorporeal life support; LCOS, low cardiac output syndrome.