Table 1.
(i) Lab tests with blood group, HLA typing, and anti-HLA antibodies | |
(ii) Assessment of vaccination status, booster injection if necessary | |
(iii) Pulmonary function tests: body plethysmography, measurement of diffusion capacity, and standardised exercise test | |
(iv) Chest CT without contrast agent, preferably not older than 6 months | |
(v) Blood gas analysis at rest | |
(vi) Current sputum culture | |
(vii) ECG, echocardiography with evaluation of pulmonary artery pressure, and right ventricular function | |
(viii) Right heart catheter if necessary | |
(ix) Assessment of nutritional status | |
(x) Abdominal sonography (including recording signs of portal hypertension), abdominal CT if necessary | |
(xi) Gastroscopy and colonoscopy if necessary | |
(xii) ENT examination, with sinus CT scan if necessary, throat and sinus swabs if necessary | |
(xiii) Bone density scan | |
(xiv) Gynaecological/urologic screening | |
(xv) Psychological assessment | |
(xvi) Dental examination | |
(xvii) Presentation at ophthalmologist | |
(xviii) Presentation at dermatologist | |
(xix) Duplex sonography of the afferent arteries if necessary | |
(xx) Peripheral closing pressure of the ankle arteries if necessary |
*Listing reflects consensus of the ECORN-CF working group. Some centres may request further investigations.