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. 2014 Apr 6;2014:230578. doi: 10.1155/2014/230578

Table 2.

Patient characteristics and the results of neuropsychological assessments.

Patient
number
Age
(years)
Gender handedness Subtype Disease duration (months) ALS FRS-R1
score
ALS FRS-R5a score HDS-R
score
STA achieved
highest stage
FAB
score
RCPM
score
1 53 F R Spinal (u) 41 3 4 30 IV 18 30
2 79 F R Spinal (l) 6 3 3 29 IV 16 27
3 61 M R Spinal (u) 24 4 3 30 IV 17 35
4 59 M R Spinal (l) 59 4 3 30 IV 18 32
5 48 M R Spinal (u) 32 4 3 30 IV 17 32
6 50 M R Spinal (l) 9 4 4 30 IV 18 33
7 74 F R Spinal (u) 21 3 3 29 IV 16 27
8 73 M R Spinal (u) 24 4 3 29 III 18 30
9 74 M R Bulbar 18 4 4 22 III 16 30
10 74 M R Spinal (l) 12 4 4 28 III 16 34
11 74 M R Bulbar 10 4 4 28 III 17 34
12 68 M R Bulbar 14 4 3 28 III 17 30
13 59 M R Spinal (u) 33 4 3 30 III 16 36
14 71 M R Bulbar 9 4 4 30 III 17 29
15 71 M R Bulbar 61 2 4 27 III 16 34
16 73 F L Bulbar 20 2 4 29 III 14 31
17 75 F R Bulbar 26 3 4 29 II 11 25
18 63 F R Bulbar 46 4 3 23 III 13 26
19 72 M R Bulbar 10 2 4 30 II 11 25
20 68 F R Spinal (u) 10 4 4 25 III 13 24
21 59 F R Spinal (u) 11 4 4 25 II 12 18
22 75 F R Spinal (u) 13 4 3 26 I 11 24
23 82 M R Bulbar 41 3 4 22 III 12 24
24 73 M R Bulbar 28 2 4 23 I 8 23
25 69 M R Spinal (u) 20 4 4 21 I 5 14

Average 67.9 23.9 3.5 3.6 27.3 14.4 28.2
SD 9.0 15.5 0.8 0.5 3.0 3.5 5.4

ALS FRS-R: revised amyotrophic lateral sclerosis functional rating scale; HDS-R: Hasegawa Dementia Scale-revised; STA: Syntax Test for Aphasia; FAB: Frontal Assessment Battery; RCPM: Raven's Coloured Progressive Matrices; R: right; L: left; (u): upper limb; (l): lower limb.