Table 2.
Patient characteristics and the results of neuropsychological assessments.
| Patient number |
Age (years) |
Gender | handedness | Subtype | Disease duration (months) | ALS FRS-R1 score |
ALS FRS-R5a score | HDS-R score |
STA achieved highest stage |
FAB score |
RCPM score |
|---|---|---|---|---|---|---|---|---|---|---|---|
| 1 | 53 | F | R | Spinal (u) | 41 | 3 | 4 | 30 | IV | 18 | 30 |
| 2 | 79 | F | R | Spinal (l) | 6 | 3 | 3 | 29 | IV | 16 | 27 |
| 3 | 61 | M | R | Spinal (u) | 24 | 4 | 3 | 30 | IV | 17 | 35 |
| 4 | 59 | M | R | Spinal (l) | 59 | 4 | 3 | 30 | IV | 18 | 32 |
| 5 | 48 | M | R | Spinal (u) | 32 | 4 | 3 | 30 | IV | 17 | 32 |
| 6 | 50 | M | R | Spinal (l) | 9 | 4 | 4 | 30 | IV | 18 | 33 |
| 7 | 74 | F | R | Spinal (u) | 21 | 3 | 3 | 29 | IV | 16 | 27 |
| 8 | 73 | M | R | Spinal (u) | 24 | 4 | 3 | 29 | III | 18 | 30 |
| 9 | 74 | M | R | Bulbar | 18 | 4 | 4 | 22 | III | 16 | 30 |
| 10 | 74 | M | R | Spinal (l) | 12 | 4 | 4 | 28 | III | 16 | 34 |
| 11 | 74 | M | R | Bulbar | 10 | 4 | 4 | 28 | III | 17 | 34 |
| 12 | 68 | M | R | Bulbar | 14 | 4 | 3 | 28 | III | 17 | 30 |
| 13 | 59 | M | R | Spinal (u) | 33 | 4 | 3 | 30 | III | 16 | 36 |
| 14 | 71 | M | R | Bulbar | 9 | 4 | 4 | 30 | III | 17 | 29 |
| 15 | 71 | M | R | Bulbar | 61 | 2 | 4 | 27 | III | 16 | 34 |
| 16 | 73 | F | L | Bulbar | 20 | 2 | 4 | 29 | III | 14 | 31 |
| 17 | 75 | F | R | Bulbar | 26 | 3 | 4 | 29 | II | 11 | 25 |
| 18 | 63 | F | R | Bulbar | 46 | 4 | 3 | 23 | III | 13 | 26 |
| 19 | 72 | M | R | Bulbar | 10 | 2 | 4 | 30 | II | 11 | 25 |
| 20 | 68 | F | R | Spinal (u) | 10 | 4 | 4 | 25 | III | 13 | 24 |
| 21 | 59 | F | R | Spinal (u) | 11 | 4 | 4 | 25 | II | 12 | 18 |
| 22 | 75 | F | R | Spinal (u) | 13 | 4 | 3 | 26 | I | 11 | 24 |
| 23 | 82 | M | R | Bulbar | 41 | 3 | 4 | 22 | III | 12 | 24 |
| 24 | 73 | M | R | Bulbar | 28 | 2 | 4 | 23 | I | 8 | 23 |
| 25 | 69 | M | R | Spinal (u) | 20 | 4 | 4 | 21 | I | 5 | 14 |
|
| |||||||||||
| Average | 67.9 | 23.9 | 3.5 | 3.6 | 27.3 | 14.4 | 28.2 | ||||
| SD | 9.0 | 15.5 | 0.8 | 0.5 | 3.0 | 3.5 | 5.4 | ||||
ALS FRS-R: revised amyotrophic lateral sclerosis functional rating scale; HDS-R: Hasegawa Dementia Scale-revised; STA: Syntax Test for Aphasia; FAB: Frontal Assessment Battery; RCPM: Raven's Coloured Progressive Matrices; R: right; L: left; (u): upper limb; (l): lower limb.