Table 2. Cardiovascular features.

	Percentage	Number	Mean age	Age range
Disease of the ascending aorta	72%	36/50	–	–
Uncomplicated dilatation >2 DS	30%	8/26	–	3–83
Preventive surgery	14%	7/50	46.0	27–58
Ascending aorta dissection	26%	13/50	46.6	30–68
Sudden death	30%	15/50	43.3	22–68
Initial abdominal aorta dissection	8%	4/50	46.3	35–56
Disease of the neck arteries	78%	14/18	–	–
Carotid arteries
Dissection	0%	0/18	–	–
Aneurysm	33%	6/18	–	–
Tortuosity	72%	13/18	–	–
Vertebral arteries
Dissection	6%	1/18	–	–
Aneurysm	22%	4/18	–	–
Tortuosity	22%	4/18	–	–
Disease of other arteries	44%	8/18	–	–
Dissection	6%	1/18	–	–
Aneurysm	39%	7/18	–	–
Tortuosity	11%	2/18	–	–