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. 2014 May 6;5(3):299S–305S. doi: 10.3945/an.113.004853

TABLE 2.

Genetic syndromes and disease states commonly presenting with obesity1

Genetic syndrome Secondary obesity
Alstrom-Wolfram (OMIM: 203800) Hypothyroidism
Bardet-Biedl (OMIM: 209900) Hypercortisolism
Beckwith-Wiedemann (OMIM: 130650) Pseudohypoparathyroidism (Albright´s hereditary osteodystrophy)
Börjesson-Forssman-Lehmann (OMIM: 301900) Neonatal hyperinsulinism
Carpenter (OMIM: 201000) Growth hormone deficiency
Cohen (OMIM: 216550) Hypothalamic obesity
Down (OMIM: 190685) Iatrogenic obesity
MEHMO (OMIM: 300148)
MOMO (OMIM:157980)
Prader-Willi (OMIM:176270)
Smith-Magenis (OMIM: 182290)
Wilson-Turner (OMIM: 309585)
WAGRO (OMIM: 612469)
1

OMIM, On-line Mendelian Inheritance in Man database (http://www.ncbi.nlm.nih.gov/sites/entrez?db = omim). MEHMO, mental retardation, epileptic seizures, hypogonadism and hypogenitalism, microcephaly, and obesity; MOMO, macrosomia, obesity, macrocephaly, and ocular abnormalities; WAGRO, Wilms tumor, anirida, genitourinary anomalies, mental regardation, and obesity syndrome.