Table 1.
Patient Characteristics | Total N=54 (%) |
Distinct N=9 (%) |
Identical N=45 (%) |
p |
---|---|---|---|---|
Female | 29 (54) | 3 (33) | 26 (58) | 0.28 |
Age, years, median [range] | 12.5 [0.03–18] | 12.9 [2–18] | 12.4 [0.03–18] | 0.47 |
CFTR mutation ΔF508 genotype a (N=45) | 43/45 (93) | 7/7 (100) | 36/38 (92) | 1.00 |
Number of cultures, median [range] | 2 [2–7] | 2 [2–5] | 2 [2–7] | 0.75 |
Includes both heterozygous (n=13) and homozygous (n=30) ΔF508 mutation CFTR mutations