Table 4.
Clinical data
| Aortic dissection | Annuloaortic ectasia | p | |
|---|---|---|---|
|
Patients |
12 |
12 |
|
|
Anthropometric (measured) |
|
|
|
| Height |
178.5 ± 10.30 |
186.2 ± 11.74 |
0.106 |
| Lower segment (cm) |
93.58 ± 9.45 |
101.9 ± 10.95 |
0.058 |
| Arm span (cm) |
186.92 ± 13.78 |
189.6 ± 15.2 |
0.656 |
| Foot size |
42.2 ± 2.5 |
44.0 ± 3.1 |
0.148 |
| Weight (kg) |
74.9 ± 14.7 |
75.0 ± 17.0 |
0.989 |
|
Anthropometric (calculated) |
|
|
|
| Upper segment (cm) |
85.0 ± 7.8 |
84.2 ± 9.9 |
0.839 |
| Body Mass Index (BMI; kg/m2) |
23.4 ± 3.70 |
21.45 ± 3.62 |
0.204 |
| Body surface area (m2) |
1.92 ± 0.22 |
1.961 ± 0.27 |
0.686 |
| Upper segment - Lower segment ratio (USLS) |
0.918 ± 0.132 |
0.838 ± 0.147 |
0.176 |
| Arm span - Height ratio (ASHR) |
1.046 ± 0.042 |
1.018 ± 0.039 |
0.092 |
|
TGF-β serum level (ng/l) |
43.78 ± 6.51 |
31.64 ± 4.99 |
<0.0001* |
|
Ghent nosology (%) |
|
|
|
| Mitral valve prolapse |
58% |
75% |
0.667 |
| Pectus carinatum |
33% |
67% |
0.220 |
| Pectus excavatum requiring surgery |
17% |
8% |
1.000 |
| Reduced upper to lower segment ratio |
33% |
50% |
0.680 |
| Increased arm span to height ratio |
58% |
17% |
0.089 |
| Wrist sign |
83% |
83% |
1.000 |
| Thumb sign |
83% |
83% |
1.000 |
| Scoliosis of > 20° or spondylolisthesis |
83% |
58% |
0.370 |
| Severe scoliosis |
58% |
42% |
0.684 |
| Reduced extension at the elbows |
17% |
8% |
1.000 |
| Medial displacement of the medial malleolus causing pes planus |
33% |
33% |
1.000 |
| Heel deformity |
8% |
17% |
1.000 |
| Pectus excavatum of moderate severity |
25% |
33% |
1.000 |
| Asymetric chest |
33% |
33% |
1.000 |
| Joint hypermobility |
75% |
42% |
0.213 |
| Highly arched palate with crowding of teeth |
58% |
42% |
0.684 |
| Facial appearance |
50% |
16% |
0.400 |
| Dolichocephaly |
25% |
17% |
1.000 |
| Enophtalmos |
8% |
8% |
1.000 |
| Retrognathia |
42% |
8% |
0.155 |
| Ectopia lentis |
25% |
17% |
1.000 |
| Myopia over 3 diopter |
8% |
17% |
1.000 |
| Increased axial length of globe |
0% |
8% |
1.000 |
| Spontaneous pneumothorax |
8% |
8% |
1.000 |
| Striae atrophicae (stretch marks) |
92% |
42% |
0.027* |
|
Positive family history (%) |
50% |
50% |
1.000 |
|
Sex (male) |
4 |
9 |
0.099 |
| Systemic score | 7 [5-8] | 7 [5.5-8] | 0.860 |
*significant data.