Table 2.
Clinical variable | Category | Number of patients (%) |
---|---|---|
Age at diagnosis | <12 months | 27 (56.25) |
13 to 36 months | 8 (16.66) | |
>36 months | 13 (27.08) | |
Onset of pulmonary symptoms | <12 months | 33 (70.21) |
13 to 36 months | 7 (14.89) | |
>36 months | 5 (10.64) | |
No clinical symptom | 2 (4.25) | |
Onset of digestive symptoms | <12 months | 32 (68.08) |
13 to 36 months | 4 (8.51) | |
>36 months | 4 (8.51) | |
Meconium ileus | 7 (14.89) | |
No clinical symptoms | 1 (2.12) | |
Age for the first infection by Pseudomonas aeruginosa | <12 months | 13 (27.66) |
13 to 36 months | 14 (29.79) | |
>36 months | 15 (31.91) | |
Without bacteria | 5 (10.64) | |
Kanga score | Non exacerbation | 38 (88.37) |
Exacerbation | 5 (11.36) | |
Shwachman-Kulczycki score | Excellent | 7 (29.16) |
Good | 7 (29.16) | |
Moderate | 8 (33.33) | |
Mild | 1 (4.16) | |
Severe | 1 (4.16) | |
Transcutaneous oxygen saturation of hemoglobin | Normal | 32 (72.72) |
Mild | 10 (22.72) | |
Moderate | 1 (2.27) | |
Severe | 1 (2.27) | |
Forced expiratory volume in first second of the FVC | Normal | 15 (51.72) |
Mild | 8 (27.59) | |
Moderate | 3 (10.34) | |
Severe | 3 (10.34) |
FVC = forced vital capacity.