Table 1. Characteristics of the patients included in the study (n = 180). a .
| Variable | Result | |
| Males | 50.00 | |
| Age, years | 17.72 ± 15.75 (0.60-24.00) | |
| Caucasoid | 91.70 | |
| Underweight and extremely underweight | 22.47 | |
| Identification of one F508del allele | 37.20 | |
| Identification of two F508del alleles | 26.70 | |
| Age at first clinical manifestations, years | 2.90 ± 8.88 (0.00-13.00) | |
| Age at diagnosis, years | 7.62 ± 13.63 (0.00-14.23) | |
| Age at first digestive symptoms, years | 3.39 ± 9.11 (0.00-12.45) | |
| Age at pulmonary symptoms, years | 2.90 ± 9.89 (0.00-13.00) | |
| SaO2, % | 94.92 ± 4.26 (66.00-99.00) | |
| Bhalla score | 8.74 ± 5.72 (0.00-25.00) | |
| Kanga score | 18.85 ± 5.84 (10.00-40.00) | |
| Shwachman-Kulczycki score | 65.85 ± 16.77 (20.00-95.00) | |
| FVC, % of predicted | 79.29 ± 23.55 (19.00-135.00) | |
| FEV1, % of predicted | 71.29 ± 27.47 (17.00-132.00) | |
| FEV1/FVC, % of predicted | 83.46 ± 15.95 (37.00-137.00) | |
| FEF25-75% | 59.05 ± 35.55 (7.00-150.00) | |
| Nasal polyps | 18.64 | |
| Diabetes mellitus | 18.64 | |
| Osteoporosis | 16.38 | |
| Pancreatic insufficiency | 79.90 | |
| Meconium ileus | 15.08 | |
| Age at first isolation of Pseudomonas aeruginosa, years | 8.55 ± 14.45 (2.00-15.00) | |
| Colonization b | ||
| P. aeruginosa | 56.42 | |
| Mucoid P. aeruginosa | 42.46 | |
| Burkholderia cepacia | 13.97 | |
| Achromobacter xylosoxidans | 10.05 | |
| Staphylococcus aureus | 78.77 | |
a
Values expressed as % or as mean ± SD (range).
b
Positive colonization based on three consecutive positive respiratory cultures in the past year