Criterion I. Pancreatic imaging (essential) |
(1) CT: Diffuse enlargement (swelling) of pancreas and (2) ERCP: Diffuse or segmental irregular narrowing of main pancreatic duct |
Criterion II. Laboratory findings |
(1) elevated levels of IgG and/or IgG4 or (2) detected autoantibodies |
Criterion III. Histopathologic findings |
Fibrosis and lymphoplasmocytic infiltration |
Criterion IV. Association of other postulated autoimmune disease |
Definite |
I+II+III+IV or I+II +III or I+II or I+III |
Probable |
Rediagnosed as “definite” if “response to the steroid” is present |
I+IV |
Possible |
I only |