. Author manuscript; available in PMC: 2015 Feb 1.

Published in final edited form as: Cerebellum. 2014 Feb;13(1):151–177. doi: 10.1007/s12311-013-0511-x

Table 3.

Cognitive/behavioral deficits observed in SCAs

SCA subtype	Deficit	Selected references
SCA1	Mental deterioration	[101–104]
	Emotional lability
	Perseveration
	Defective verbal memory
	Executive dysfunction
SCA2	Dementia	[105–108]
	Executive dysfunction
	Impairment of verbal memory
	Impulsiveness
	Anxiety
	Depression
SCA3	Executive dysfunction	[109–113]
	Impairment of verbal memory
	Depression
	Apathy
SCA6	Slight evidence of defective verbal memory and verbal fluency	[114]
SCA13	Non progressive mental retardation	[115]
SCA17	Prominent psychiatric and behavioural symptoms	[95]
SCA17	Executive dysfunction	[95]
DRPLA	Dementia	[116]
	Seizures
	Psychiatric symptoms

Only SCAs with detailed neuropsychological reports are considered