Table 1.

Patient characteristics at presentation

Clinical characteristic	Number of patients (%)
Median age, years	38 (range 21–64)
Sex (n = 15)
Female	6 (40)
Male	9 (60)
History of immunocompromise	4 (27)
Sjogren's disease, on intermittent prednisolone, methotrexate	1 (7)
Crohn's disease, on chronic mercaptopurine	1 (7)
Ulcerative colitis, chronic mercaptopurine, and mesalamine	2 (13)
Sites of involvement
Bone marrow	15 (100)
Splenomegaly	15 (100)
Liver involvement	10 (67)
Hepatomegaly	6 (40)
Biopsy-proven liver involvement in patients without hepatomegaly	3 (20)
Abnormal LFTs	6 (40)
Adenopathy	2 (13)
Peripheral blood involvement	4 (27)
B symptoms
Fever	10 (67)
Night sweats	9 (60)
Weight loss	8 (53)
Cytopenias
Anemia	8 (73)
Thrombocytopenia	7 (64)
Neutropenia	4 (36)

LFTs, liver function tests.