Table 4.
CMR data in controls and in asymptomatic versus symptomatic Duchenne carriers
|
Variables |
Controls |
Asymptomatic |
Between DMDc p< |
Symptomatic |
F |
p< |
|---|---|---|---|---|---|---|
| (n = 37) | (n = 21) | (n = 9) | ||||
| LGE quantity (ml) |
0 |
0.76 ± 0.17 |
0.05 |
1.77 ± 0.27 |
19.6 |
0.0001 |
| Percent LGE versus LV mass (%) |
0 |
0.68 ± 0.17 |
0.02 |
1.86 ± 0.26 |
22.1 |
0.0001 |
| LGE location |
|
|
|
|
|
|
| Sub-endocardial |
0 |
0 |
- |
0 |
- |
|
| Mid-myocardial |
0 |
0.14 ± 0.05 |
0.02 |
0.56 ± 0.09 |
15.1 |
0.0001 |
| Sub-epicardial |
0 |
0.33 ± 0.07 |
0.57 |
0.44 ± 0.11 |
10.7 |
0.0001 |
| Topographic distribution |
|
|
|
|
|
|
| Segment 4 |
0 |
0.14 ± 0.05 |
0.08 |
0.44 ± 0.09 |
9.8 |
0.0002 |
| Segment 5 |
0 |
0.33 ± 0.07 |
0.09 |
0.67 ± 0.11 |
18.3 |
0.0001 |
| Segment 6 |
0 |
0.29 ± 0.07 |
0.05 |
0.67 ± 0.10 |
18.1 |
0.0001 |
| Segment 10 |
0 |
0.05 ± 0.04 |
0.15 |
0.22 ± 0.07 |
4.5 |
0.05 |
| Segment 11 |
0 |
0.09 ± 0.05 |
0.11 |
0.33 ± 0.08 |
6.9 |
0.01 |
| Segment 12 | 0 | 0.14 ± 0.06 | 0.24 | 0.33 ± 0.08 | 6.2 | 0.01 |
DMDc = Duchenne muscular dystrophy carriers. Data are mean ± standard errors.