Table 2.

Full-Field Electroretinographic Findings in Left Eyes of Family Members Carrying KLHL7 Mutations

			31-Hz Flicker
Age, y	Rod Response,µV	Maximal Response, µV	Amplitude, µV	Annual Loss, %	31-Hz Implicit Time, ms
A-III-3
76	NDa	NDa	NDb	NA	NA
A-IV-1				0.5
50	9.0	NAc	29		34
62	7.0	81	26		37
65	4.6	61	27		36
A-IV-2				6.0
45	4.3	34	17		38
56	NDa	19	6		39
59	NDa	14	3		33
B-III-3				3.0
59	3.7	30	NA		NA
60	2.9	27	NA		NA
61	NDa	28	4		40
62	NDa	35	2		43
63	NDa	21	NA		NA
74	NDa	10	3		42
C-III-1
35	NDa	45	25	NA	38

Abbreviations: NA, not available; ND, nondetectable.

^aNondetectable at criterion amplitude of 3.0 µV.

^bNondetectable at criterion amplitude 0.1 µV.

^cData unavailable at International Society for Clinical Electrophysiology of Vision standard flash intensity.