Table 1.
Demographic Information
Group/Diagnosis | N | Median Age (yr) (range) | No. of Females | No. of Males |
---|---|---|---|---|
All patients | 123 | 12.1 (0.6-75.7) | 67 | 56 |
<18 yr | 75 | 7.2 (0.6-17.9) | 34 | 41 |
<6 yr | 31 | 2.2 (0.6-5.6) | 14 | 17 |
A | 63 | 11.3 (1.1-69.1) | 34 | 29 |
Idiopathic | 22 | 28.5 (2.1-69.1) | 16 | 6 |
Cyclic | 10 | 10.7 (2.5-47.2) | 5 | 5 |
Congenital* | 31 | 7.7 (1.1-32.9) | 13 | 18 |
Kostmann’s syndrome | 20 | 7.6 (1.1-19.1) | 7 | 13 |
B | 60 | 14.0 (0.6-75.7) | 33 | 27 |
Idiopathic | 20 | 30.8 (1.3-75.7) | 12 | 8 |
Cyclic | 11 | 27.4 (10.5-59.1) | 8 | 3 |
Congenital* | 29 | 8.0 (0.6-33.8) | 13 | 16 |
Kostmann’s syndrome | 16 | 5.3 (0.6-33.8) | 6 | 10 |
Congenital neutropenia includes patients with Shwachmann-Diamond syndrome (3). myelokathexis (4). glycogen storage disease type lb (1). possible autoimmune neutropenia (1), and neutropenia with dysgammaglobulinemia (1).