Table 2.
Percentages of patients with CCCs classified by CCC v1 versus CCC v2 in KID 2009 and NEDS 2010
|
CCC categories |
KID* (Weighted N = 7,337,017) |
NEDS (Weighted N = 29,741,986) |
||||
|---|---|---|---|---|---|---|
| CCC v1 | CCC v2 | % Change | CCC v1 | CCC v2 | % change | |
| Neurologic and neuromuscular |
1.36 (1.35–1.37) |
2.28 (2.26–2.30) |
67.64% |
0.31 (0.26–0.37) |
0.52 (0.43–0.61) |
67.74% |
| Cardiovascular |
3.29 (2.27–3.30) |
2.32 (2.30–2.33) |
–29.48% |
0.43 (0.38–0.48) |
0.48 (0.42–0.54) |
11.63% |
| Respiratory |
0.92 (0.91–0.93) |
0.97 (0.96–0.98) |
5.43% |
0.08 (0.07–0.11) |
0.13 (0.10–0.16) |
62.50% |
| Renal and urologic |
0.75 (0.74–0.76) |
1.21 (1.12–1.22) |
61.33% |
0.08 (0.07–0.10) |
0.13 (0.11–0.15) |
62.50% |
| Gastrointestinal |
0.62 (0.61–0.63) |
2.02 (2.00–2.03) |
225.81% |
0.09 (0.08–0.10) |
0.39 (0.30–0.48) |
333.33% |
| Hematologic or immunologic |
1.32 (1.30–1.33) |
1.60 (1.58–1.61) |
21.21% |
0.34 (0.28–0.39) |
0.41 (0.35–0.47) |
20.59% |
| Metabolic |
0.84 (0.83–0.85) |
1.11 (1.10–1.12) |
32.14 |
0.14 (0.12–0.16) |
0.19 (0.16–0.21) |
35.71% |
| Other congenital or genetic defect |
1.64 (1.63–1.65) |
1.64 (1.63–1.65) |
0.00% |
0.31 (0.27–0.36) |
0.31 (0.27–0.36) |
0.00% |
| Malignancy |
2.10 (2.08–2.11) |
1.64 (1.63–1.65) |
–21.91% |
0.21 (0.17–0.25) |
0.16 (0.12–0.20) |
-23.81% |
| Neonatal |
--- |
1.14 (1.13–1.15) |
--- |
--- |
0.03 (0.02–0.04) |
--- |
| Technology dependency |
--- |
2.64 (2.62–2.65) |
--- |
--- |
0.46 (0.35–0.58) |
--- |
| Transplantation |
--- |
0.38 (0.37–0.38) |
--- |
--- |
0.05 (0.04–0.07) |
--- |
| CCC (Any CCC) | 10.56 (10.53–10.59) | 11.57 (11.53–11.59) | 9.56% | 1.83 (1.60–2.06) | 2.27 (1.97–2.72) | 24.04% |
Legend: Data presented as percentage (% (95% CI) ). CCCv2 is classified using ICD-9. * Included all KID patients.