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. Author manuscript; available in PMC: 2015 Sep 1.
Published in final edited form as: Am J Med Genet A. 2014 Jun 11;164(9):2217–2225. doi: 10.1002/ajmg.a.36628

Table IIb.

Skin and Nail Findings in WS

# With
feature/
# assessed
Percentage Comment
Soft skin 40/48 83%
Presence of a Scar 30/50 60% 18/30 are surgical
Mildly abnormal scar
if scar present
15/30 50%
Markedly abnormal scar
if present
10/30 33%
Forehead wrinkling 20/47 43%
Peri-ocular wrinkling 39/48 81%
Peri-oral wrinkling 30/49 61%
Nail biting and/or skin
picking
21/50 42% 19 current; + 2 with
history.
Keratosis pilaris 20/50 40% Most cases mild
Atrophic areas of skin 14/50 34%
Stretch Marks 10/50 20% 4/10 with normal/low BMI
Dry skin / Hyperkeratosis 10/50 20% Most cases mild