Table 2.
Characteristics | n | (%) | |
---|---|---|---|
Mode of inheritance | Autosomal recessive | 12 | 26.7% |
Autosomal dominant | 6 | 13.3% | |
Sporadic | 27 | 60.0% | |
ERG | Subnormal | 2 | 4.4% |
Non-recordable | 43 | 95.6% | |
Mean | SD | ||
Estimated age of onset | (Years old) | 27.4 | 16.9 |
Estimated duration | (Years) | 17.6 | 14.3 |
Abbreviations: ERG, electroretinogram; SD, standard deviation.