Table 3.
Results: 27 months analysis | N | % |
---|---|---|
Patients died |
15 |
11.5% |
Dropouts |
4 |
3.0% |
CTEPH/CTPVD with exercise PH* |
8/3 |
6.2%/2.3% |
CTEPH/CTPVD: “CPET pos and Echo neg“# | 2/1 | 1.5/0.77% |
*In 8 patients pathological imaging and mean pulmonary artery pressure (mPAP) at rest of ≥ 25 mmHg had been found. In 3patients pathological imaging, mPAP at rest of < 25 mmHg, but increasing mPAP under exercise without increasing pulmonary artery occlusion pressure had been found suggesting CTPVD with exercise induced PH. # 2 out of 8 (25%) patients diagnosed with CTEPH and 1 out of 3 (33%) patients diagnosed with CTPVD and exercise induced PH showed normal echocardiography, but findings in the cardiopulmonary exercise test suspicious for functional relevant pulmonary perfusion abnormalities.