Table 1 . Different diagnostic criteria of FMF.

Major Criteria

Typical Attacks

1. Peritonitis (generalized)

2. Pleuritic (unilateral) or pericarditis

3. Monoarthritis (hip, knee, ankle)

4. Fever alone

5. Favorable response to colchicine

Minor Criteria

Incomplete attacks involving one or more of the following sites

1. Abdomen

2. Chest

3. Joint

4. Exertional leg pain

Supportive Criteria

1. Family history of FMF

2. Appropriate ethnic origin

3. Age <20 years at disease onset

4. Features of attacks: I. Severe, requiring bed rest II. Spontaneous remission III. Symptom-free interval IV. Transient inflammatory response, with one or more abnormal test result(s) V. White blood cell count, erythrocyte sedimentation rate, serum amyloid A, and/or fibrinogen

5. Episodic proteinuria/hematuria

6. Unproductive laparotomy or removal of white appendix

7. Consanguity of parents