Table 1.
Details of HSCR patients with associated congenital heart diseases.
| Patient | Sex | Age (m) | Type of aganglionosis | Type of heart disease | Management | Syndrome |
|---|---|---|---|---|---|---|
| 1 | M | 59 | S-HSCR | Small OS ASD + small PDA | F-UP | |
| 2 | M | 58 | S-HSCR | Small OS ASD + small PM VSD | F-UP | Down |
| 3 | F | 54 | S-HSCR | Small OS ASD | F-UP | |
| 4 | M | 51 | S-HSCR | Large OS ASD + moderate PM VSD | SP | |
| 5 | F | 309 | S-HSCR | Large OP ASD | SP | Down |
| 6 | M | 171 | S-HSCR | Large OS ASD + moderate PM VSD | SP | Down |
| 7 | M | 192 | TCA | Large PM VSD | SP | Down |
| 8 | F | 27 | TCA | AC | SP | Turner |
| 9 | M | 96 | S-HSCR | Moderate size OS ASD | SP | |
| 10 | M | 52 | S-HSCR | Small PDA | F-UP | Down |
| 11 | M | 107 | S-HSCR | Small PDA | F-UP |
M, male; F, female; m, months of life at time of cardiac screening; S-HSCR, short segment Hirschsprung’s disease; TCA, total colonic aganglionosis; OS, ostium secundum; OP, ostium primum; ASD, atrial septal defect; PM VSD, perimembranous ventricular septal defect; AC, aortic coarctation; PDA, patent ductus arteriosus; F-UP, follow up; SP, surgical procedure.