Table 1.
Baseline clinical and hemodynamic data (n = 54)
| Age (years) | 44 ± 12 |
|---|---|
| Sex (f/m) | 45/9 |
| Etiology n (%) | |
| Idiopathic | 37 (68) |
| Associated to | |
| Schistosomiasis | 7 (13) |
| CTD | 8 (15) |
| CHD | 2 (4) |
| NYHA functional class n (%) | |
| II | 14 (26) |
| III | 28 (52) |
| IV | 12 (22) |
| 6MWT (m) | 418 ± 121 |
| mPAP (mmHg) | 64 ± 17 |
| PAOP (mmHg) | 10 ± 2 |
| Cardiac output (L/min) | 4 ± 1 |
| PVR (WU) | 15 ± 8 |
| Therapy n (%) | |
| ERA | 46 (85) |
| PDE-5 inhibitors | 8 (15) |
CTD Connective tissue disease, CHD Congenital heart disease, NYHA New York Heart Association, 6MWT Length in non-encouraged six-minute-walk test, RAP Right Atrial Pressure, mPAP Mean Pulmonary Artery Pressure, PAOP Pulmonary Artery Occlusion Pressure, PVR Pulmonary Vascular Resistance, ERA Endothelin Receptor Antagonists, PDE-5 Phosphodiesterase-5 inhibitor.