Table 2. Baseline data: Bodyplethysmography including mouth occlusion pressure and echocardiography.
| N | Baseline (Mean ± SD) | |
| Bodyplethysmography | ||
| VC (% pred.) | 74 | 100.4±15.6 |
| FEV1 (% pred.) | 74 | 99.8±17.7 |
| FEV1/VC (%) | 74 | 79.2±7.7 |
| MEF 25 (% pred.) | 74 | 71.9±28.6 |
| ITGV (% pred.) | 74 | 91.2±16.5 |
| RV (% pred.) | 74 | 102.1±32.7 |
| TLC (% pred.) | 74 | 102.0±12.2 |
| TLC-He (% pred) | 30 | 90.0±11.0 |
| SR tot (% pred.) | 74 | 109.1±63.5 |
| TLCO SB (% pred.) | 47 | 87.3±14.0 |
| P0.1 (kPa) | 51 | 0.28±0.13 |
| PI max (kPa) | 36 | 6.8±2.9 |
| P0.1/PI max | 29 | 0.05±0.05 |
| BF (1/min) | 35 | 18.0±5.5 |
| Echocardiography | ||
| IVSd (mm) | 54 | 10.9±2.5 |
| LVPWd (mm) | 54 | 10.6±2.3 |
| EF biplan Simpson (%) | 53 | 63.1±7.2 |
| LIMP | 46 | 0.54±0.28 |
| MAPSE (cm) | 51 | 1.8±0.4 |
| E/E’ | 54 | 6.74±1.67 |
| TAPSE (mm) | 54 | 28.8±5.1 |
| RIMP | 51 | 0.40±0.22 |
| RA area (cm2) | 54 | 13.9±5.5 |
| RV (cm) | 54 | 3.2 0.7 |
| e/e’ | 51 | 4.82±1.67 |
| TDI-TVA (cm/s) | 51 | 14.5±3.0 |
| RVSP (mmHg) | 7 | 20.4±8.6 |
| PV AccT (ms) | 50 | 117.8±29.6 |
Data are shown as mean ± standard deviation.