Skip to main content
. Author manuscript; available in PMC: 2015 May 1.
Published in final edited form as: Br J Ophthalmol. 2014 Jan 31;98(5):709–711. doi: 10.1136/bjophthalmol-2013-304822

Figure 2. Visual Function.

Figure 2

A. Electroretinography. Replicated dual ERG tracing of the proband, affected brother, and mother (manifest carrier) were compared to a normal subject. The traces showed implicit time delays and amplitude reduction in the cone system with a relatively normal rod system. The carrier female ERG showed asymmetry where the right eye was more affected and corresponded with the fundus findings. B – E. Goldmann visual fields. Visual field testing showed that both the proband (B, C) and the affected brother (D, E) had central scotomas with a small island of preservation inside central scotoma of both eyes. Minimal visual field constrictions were also noted in both patients.

HHS Vulnerability Disclosure