Table 1.

Diagnostic criteria for NF2[22]

Definite NF2
1	Bilateral vestibular schwannomas or
2	Family history of NF2 (first-degree family relative) plus
	a Unilateral vestibular schwannoma at age < 30 yr, or
	b Any two of the following: meningioma, glioma, schwannoma or juvenile posterior subcapsular lenticular opacities/juvenile cortical cataract
Presumptive or probable NF2
1	Unilateral vestibular schwannoma at age < 30 yr plus at least one of the following: meningioma, glioma, schwannoma or juvenile posterior subcapsular lenticular opacities/juvenile cortical cataract
2	Multiple meningiomas (two or more) plus
	a Unilateral vestibular schwannoma at age < 30 yr, or
	b One of the following: glioma, schwannoma or juvenile posterior subcapsular lenticular opacities/juvenile cortical cataract