Table 2.
Clinical manifestation of CVID patients
| Subjects | LPS | Autoimmunity | IBD | Lymphoid hyperplasia | Granulomatous disease |
| CVID-1 | No | No | No | Yes (intestinal) | No |
| CVID-2 | Yes | No | No | No | No |
| CVID-3 | Yes | No | No | No | No |
| CVID-4 | Yes | No | No | No | No |
| CVID-5 | Yes | Yes | No | Yes (intestinal) | Yes |
| CVID-6 | No | No | No | No | No |
| CVID-7 | No | No | No | No | No |
| CVID-8 | No | No | No | No | No |
| CVID-9 | Yes | Yes | No | No | Yes |
| CVID-10 | No | No | No | No | No |
| CVID-11 | Yes | No | No | Yes (intestinal) | No |
| CVID-12 | Yes | Yes | No | No | No |
| CVID-13 | No | Yes | Yes | Yes (intestinal) | Yes |
| CVID-14 | Yes | Yes | No | No | Yes |
| CVID-15 | Yes | Yes (diabetes) | No | Yes (intestinal) | No |
| CVID-16 | Yes | No | No | Yes (intestinal) | No |
| CVID-17 | No | No | No | Yes (intestinal) | No |
| CVID-18 | No | No | No | Yes (intestinal) | No |
| CVID-19 | Yes | No | No | Yes (intestinal) | No |
| CVID-20 | Yes | No | No | Yes (intestinal) | No |
| CVID-21 | Yes | No | No | Yes (intestinal) | No |
| CVID-22 | No | No | No | Yes (intestinal) | No |
| CVID-23 | No | No | No | Yes (intestinal) | No |
| CVID-24 | No | No | No | Yes (intestinal) | No |
| CVID-25 | No | No | No | Yes (intestinal) | No |
| CVID-26 | No | Yes (diabetes) | No | Yes (intestinal) | No |