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. 2014 Aug 8;289(39):26709–26721. doi: 10.1074/jbc.M114.586156

TABLE 1.

Lysosomal enzyme activities (nmol/min/ml) in blood sera of wild-type, heterozygote (nym/+), and nym (nym/nym) mouse

Lysosomal enzyme Wild type (+/+) nym/+ nym/nym
β-Hexosaminidase (nmol/min/ml) 86.94 ± 7.32 144.02 ± 7.21 1094.69 ± 68.90
β-Mannosidase (nmol/min/ml) 10.49 ± 0.57 11.88 ± 1.76 29.07 ± 1.84
α-Mannosidase (nmol/min/ml) 50.30 ± 4.12 119.13 ± 7.23 1433.02 ± 144.98
β-Glucoronidase (nmol/min/ml) 6.96 ± 0.54 6.43 ± 1.06 28.88 ± 6.46
β-Galactosidase (nmol/min/ml) 8.13 ± 1.24 6.98 ± 0.93 63.58 ± 7.30
α-Galactosidase (nmol/min/ml) 2.12 ± 0.25 1.90 ± 0.13 2.20 ± 0.13
Glucocerebrosidase (pmol/min/ml) 3.31 ± 0.4 3.36 ± 0.45 3.47 ± 0.28