TABLE 2.
Lysosomal enzyme | Wild type (+/+) | nym/nym |
---|---|---|
β-Hexosaminidase (nmol/mg/h) | 1.39 ± 0.19 | 2.24 ± 0.22 |
β-Mannosidase (nmol/mg/h) | 0.71 ± 0.09 | 0.70 ± 0.09 |
α-Mannosidase (nmol/mg/h) | 0.47 ± 0.07 | 0.70 ± 0.02 |
β-Glucoronidase (nmol/mg/h) | 0.54 ± 0.07 | 0.87 ± 0.05 |
β-Galactosidase (nmol/mg/h) | 1.60 ± 0.24 | 0.99 ± 0.10 |
α-Galactosidase (pmol/mg/h) | 42.42 ± 11.57 | 45.34 ± 3.41 |
Glucocerebrosidase (pmol/mg/h) | 16.70 ± 3.96 | 16.98 ± 5.97 |