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. 2014 Aug 8;289(39):26709–26721. doi: 10.1074/jbc.M114.586156

TABLE 2.

Lysosomal enzyme activities (nmol/mg/h) in brain lysate of wild-type and nym (nym/nym) mouse

Lysosomal enzyme Wild type (+/+) nym/nym
β-Hexosaminidase (nmol/mg/h) 1.39 ± 0.19 2.24 ± 0.22
β-Mannosidase (nmol/mg/h) 0.71 ± 0.09 0.70 ± 0.09
α-Mannosidase (nmol/mg/h) 0.47 ± 0.07 0.70 ± 0.02
β-Glucoronidase (nmol/mg/h) 0.54 ± 0.07 0.87 ± 0.05
β-Galactosidase (nmol/mg/h) 1.60 ± 0.24 0.99 ± 0.10
α-Galactosidase (pmol/mg/h) 42.42 ± 11.57 45.34 ± 3.41
Glucocerebrosidase (pmol/mg/h) 16.70 ± 3.96 16.98 ± 5.97