Table 1.

Diagnostic criteria for familial Mediterranean fever [3]

Major criteria: typical attack*	Minor criteria
1. Peritonitis (generalized)	1. Incomplete attacks affecting one or more sites
2. Pleurisy (unilateral) or pericarditis	-Abdomen
3. Monoarthritis (hip, knee, ankle)	-Lungs
4. Isolated fever	-Joints
*axillary temperature >38°C, duration 12–72 h and ≥ three attacks	2. Exertion-related leg pain
	3. Response to colchicine

The diagnosis requires at least one major criteria or at least two minor criteria.