Table 1. Skeletal muscle metabolites - 13C NMR spectroscopy.
Subjects | Glycogen (mM) | Total Creatine (mM) | Glycogen/Total Creatine |
MD | 192.5±15.1 | 85.6±22.5 | 2.3±0.6 |
PFKD | 202.1 | 124.2 | 1.6 |
Controls | 75.7±13.6 | 77.1±8.3 | 1.0±0.3 |
Values are expressed individually or group means ± SD. MD, McArdle disease; PFKD, phosphofructokinase deficiency; mM, millimoles per liter.