Table 1.

Patients whose skin fibroblasts were studied. BMI, Body Mass Index; FVC%, residual forced vital capacity; ALSFRS-R, ALS functional rating scale; Riluzole, number of patients who were receiving treatment at the time of skin biopsy. For Age of onset and age at biopsy, ALSFRS-R, BMI, and FVC% numbers represent averages ± standard deviations.

	ALS	PLS	CTL
Number	50	35	50
Sex	25 F, 25 M	16 F, 19 M	25 F, 25 M
Age of Onset	59 ± 10.23	52 ± 8.33	N/A
Age at Biopsy	60 ± 10.14	59 ± 8.62	60 ± 8.55
Presentation	16 Bulbar, 34 Limb	9 Bulbar, 25 Limb	N/A
ALSFRS-R	33 ± 8.92	33 ± 5.91	N/A
BMI	26 ± 5.7	27 ± 4.1	N/A
FVC %	75 ± 27.6	89 ± 21.7	N/A
Riluzole	27	1	0