Table 1. Clinical findings of all affected males.
Patient No. | Age of onset (a) | Age of diagnosis (a) | BCVA OD/OS | Fundus change | Visual field | ERG recordings |
11 | 13 | 53 | HM/HM | Light yellow appearance of optic disk; pigment deposit; retinal vessel attenuation | Tubular visual field | Reduced |
15 | 15 | 40 | 0.02/0.02 | Tigroid fundus; light yellow appearance of optic disk; pigment deposit; Retinal vessel attenuation | Tubular visual field | Reduced |
20 | 12 | 42 | 0.04/0.04 | Light yellow appearance of optic disk; pigment deposit; retinal vessel attenuation | Tubular visual field | Reduced |
27 | 13 | 47 | 0.01/0.01 | Light yellow appearance of optic disk; pigment deposit; retinal vessel attenuation. | Tubular visual field | Reduced |
BCVA: Best correct visual acuity; OD: Right eye; OS: Left eye; HM: Hand motion; ERG: Electroretinograms.