Table 1.
Author | Age (yrs) (at event) |
Gender | Clinical history and prebleeding therapies | Antibody profile |
Site of bleeding(s) | Treatment | Outcome (as reported) |
---|---|---|---|---|---|---|---|
Orrell et al. [7] | 50 | Female | DM age 34 Corticosteroid Azathioprine IVIG |
None specified | Left rectus abdominis | Blood transfusions Prednisone Azathioprine | Survived, no recurrent bleeding |
| |||||||
Orrell et al. [7] | 11 | Female | DM age 8 Prednisone |
ANA 1 : 320 speckled |
Retroperitoneum, posterior to right ascending colon |
Supportive | Survived without recurrence |
| |||||||
Fang et al. [8] | 65 | Female | PM age 65 Hydrocortisone Prednisone |
ANA 1 : 320 speckled |
Retroperitoneum, superior duodenal pancreatic artery, SMA |
Angiography with embolization | Expired from sepsis without rebleeding |
| |||||||
Yamagishi et al. [9] | 64 | Female | DM/ILD age 64 Solumedrol Prednisone Cyclosporine Dalteparin |
ANA positive Elevated serum KL-6 |
Retroperitoneum, right psoas, right iliacus, left rectus sheath |
Angiography with embolization with rebleeding and repeat embolization | Expired from TTP and multiorgan failure |
| |||||||
Higashi et al. [10] | 77 | Female | DM age 77 Solumedrol Prednisone Cyclosporine Heparin |
Elevated serum KL-6 |
Retroperitoneum, left iliopsoas, left iliacus, right sternomastoid |
Supportive | Expired from DIC |
| |||||||
Van Gelder et al. | 50 | Male | DM/ILD age 50 Solumedrol IVIG |
Anti-Ro52 | Retroperitoneum, right iliacus, right psoas |
Transfusions Solumedrol |
Expired from multiorgan failure |
| |||||||
Van Gelder et al. | 63 | Female | DM/ILD age 63 Solumedrol IVIG |
Anti-SSA Anti-Ro52 |
Retroperitoneum, right pectineus, right iliopsoas |
Transfusions Solumedrol Cytoxan |
Expired from multiorgan failure |