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. Author manuscript; available in PMC: 2015 May 30.
Published in final edited form as: J Proteomics. 2014 Apr 5;103:178–193. doi: 10.1016/j.jprot.2014.03.037

Table 4.

Identified DRM proteins associated with deafness

Gene Name Gene Description Deafness
ACTG1 Cytoplasmic/Cytoskeletal Actin, Gamma 1 Non-Syndromic
CISD2 CDGSH Iron Sulfur Domain 2 Non-Syndromic
CLCNKB Chloride Channel, Voltage-Sensitive Kb Syndromic
GJA1 Connexin 43 Non-Syndromic
GJB6 Connexin 30 Non-Syndromic
KCNQ1 Voltage-gated Potassium Channel Syndromic
MYH9 Myosin, Heavy Chain 9, non-muscle Non-Syndromic
MYO6 Myosin 6 Non-Syndromic
OTOA Otoancorin Non-Syndromic
SLC12A2 Basolateral Na+-K+-Cl Symporter Syndromic
TECTA Tectorin Alpha Non-Syndromic