Table 2. Patients’ classification according to the updated classification of pulmonary hypertension, Nice 2013 (12).

Classification of PH	n	%
Group 1
1-1 IPAH	26	17.5
1-3 Drugs and toxins induced PAH	5	3
1-4
1-4-1 Connective tissue disease	22	15
1-4-2 Human immunodeficiency virus infection	7	5
1-4-3 Portal hypertension	13	9
1-4-4 Congenital heart disease	42	28
1-4-4-1 Eisenmenger syndrome	30	20
1-4-4-4 Closed-shunt associated with PAH	12	8
Group 4 Chronic thromboembolic pulmonary hypertension	20	13.5
Group 5 PH with unclear and/or multifactorial mechanisms	14	9.5

n, number of patients; PAH, pulmonary arterial hypertension; PH, pulmonary hypertension.